United Kingdom survey of current management of juvenile localized scleroderma
نویسندگان
چکیده
منابع مشابه
United Kingdom survey of current management of juvenile localized scleroderma.
OBJECTIVES Juvenile localized scleroderma (JLS) is a rare condition that is often difficult to assess and for which a variety of monitoring tools have been described. We aimed to describe how monitoring tools are used and perceived by clinicians in the UK, to ascertain treatments used for JLS and to provide a description of transition arrangements to adult care. METHODS An e-survey of UK paed...
متن کاملPReS-FINAL-2119: United Kingdom survey of current management of juvenile localised scleroderma
Results 48 clinicians (35 dms, 13 prs) from across the UK responded. At time of survey response, dms reported managing a mean 4.2 CYP with JLS; prs 17.9. 26% dms managed all CYP in collaboration (with a PR, paediatrician, adult rheumatologist or another DM) whilst 31% prs managed all CYP in collaboration (with a DM or paediatrician). 43% of dms and 91% prs reported formal transition arrangement...
متن کاملJuvenile localized scleroderma: review of 44 patients
Results 70.5% of patients were females. CM (34.1%) and LM (34.1%) were the most frequently subtypes. Mean age at first symptoms was 7.7 years (Figure 1). Medium time between first signs/symptoms and diagnosis was 15.42 months. One patient with CM head-neck lesions had Parry-Romberg disease with neurological involvement. 50% of patients with head-neck LM had “coup de sabre” subtype, 25% of that ...
متن کاملSurgical Management of Localized Scleroderma
BACKGROUND Localized scleroderma is characterized by a thickening of the skin from excessive collagen deposits. It is not a fatal disease, but quality of life can be adversely affected due to changes in skin appearance, joint contractures, and, rarely, serious deformities of the face and extremities. We present six cases of localized scleroderma in face from our surgical practice. METHODS We ...
متن کاملDietary management of hepatic encephalopathy in cirrhotic patients: survey of current practice in United Kingdom.
In the early 1950s it was shown that some patients with cirrhosis given “nitrogenous substances,” including excess dietary protein, developed hepatic “precoma.” 1 These largely uncontrolled observations led to the introduction of dietary protein restriction to treat hepatic encephalopathy. Recent research has shown, however, that protein requirements are increased in these patients, that high p...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Rheumatology
سال: 2014
ISSN: 1462-0324,1462-0332
DOI: 10.1093/rheumatology/keu212